Table Of ContentDefects of Secretion
in Cystic Fibrosis
ADVANCES IN EXPERIMENTAL MEDICINE AND BIOLOGY
Editorial Board:
NATHAN BACK, State University of New York at Buffalo
IRUN R. COHEN, The Weizmann Institute of Science
DAVID KRITCHEVSKY, Wistar Institute
ABEL LAJTHA, A^. S. Kline Institute for Psychiatric Research
RODOLFO PAOLETTI, University of Milan
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Defects of Secretion
in Cystic Fibrosis
Edited by
Carsten Schultz
European Molecular Biology Laboratory
Heidelberg, Germany
Sprrii nger
Library of Congress Cataloging-in-Publication Data
Defects of secretion in cystic fibrosis/edited by Carsten Schultz.
p. ; cm. — (Advances in experimental medicine and biology; v. 558)
Includes bibliographical references and index.
ISBN 0-387-23076-9 (alk. paper)
1. Cystic fibrosis—Pathophysiology. 2. Cystic fibrosis—Molecular aspects. I. Schultz,
Carsten. II. Series.
[DNLM: 1. Cystic Fibrosis—physiopathology—Congresses. 2. Cystic
Fibrosis—therapy—Congresses. 3. Cystic Fibrosis Transmembrane Conductance
Regulator—Congresses. 4. Pancreas—secretion—Congresses. WI 820 D313 2005]
RC858.C95D44 2005
616.372—dc22
2004063217
ISBN: 0-387-23076-9
elSBN: 0-387-23250-8
©2005 Springer Science+Business Media, Inc.
All rights reserved. This work may not be translated or copied in whole or in part without the written
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Acknowledgments
I would like to thank Sylke Helbing and Bettina Schafer for editorial help
and Nicole Heath for critically reading through part of the manuscripts. I
also would like to acknowledge all speakers and participants of the 'Defects
of Secretion' symposium held in Heidelberg in November 2003. Your
contributions and lively discussions made the compilation of this book worth
while.
Contributing Authors
Gabriele Adam
Universitat Regensburg, Germany
Susan J. Anderson
University of Alabama at Birmingham, AL, USA
Tanja Bachhuber
Universitat Regensburg, Germany
Dale J. Benos
University of Alabama at Birmingham, AL, USA
Christoph Bohmer
Eberhard-Karls-Universitat Tubingen, Germany
Horst Fischer
Children's Hospital Oakland Research Institute, Oakland, CA, USA
Catherine M. Fuller
University of Alabama at Birmingham, AL, USA
Sherif Gabriel
University of North Carolina, Chapel Hill, NC, USA
Erich Gulbins
Eberhard-Karls-Universitat Tubingen, Germany
1 CONTRIBUTING AUTHORS
Gunnar C. Hansson
Goteborg University, Gothenburg, Sweden
Jean-Daniel Horisberger
University Lausanne, Switzerland.
Beate lUek
Children's Hospital Oakland Research Institute, Oakland, CA, USA
Malin E. V. Johansson
Goteborg University, Gothenburg, Sweden
Reinhard Kandolf
Eberhard-Karls-Universitat Tubingen, Germany
RolfK.-H.Kinne
Max-Planck-Institut fur molekulare Physiologie, Dortmund, Germany
Helmut Kipp
Max-Planck-Institut fiir molekulare Physiologie, Dortmund, Germany
Karin Klingel
Eberhard-Karls-Universitat Tubingen, Germany
Gergely Kovacs
University of Alabama at Birmingham, AL, USA
Karl Kunzelmann
Universitat Regensburg, Germany
Florian Lang
Eberhard-Karls-Universitat Tubingen, Germany
Albrecht Lepple-Wienhues
Eberhard-Karls-Universitat Tubingen, Germany
Martin E. Lidell
Goteborg University, Gothenburg, Sweden
Marcus Mall
The University of North Carolina, Chapel Hill, NC, USA
CONTRIBUTING AUTHORS
Mark Moody
Inologic Inc., Seattle, WA, USA
Bettina Murle
Universitat Regensburg, Germany
Paul M. Quinton
UCSD School of Medicine, La JoUa, CA, USA
Monica Palmada
Eberhard-Karls-Universitat Tubingen, Germany
Caria M. Pedrosa Ribeiro
The University of North Carolina, Chapel Hill, NC, USA
Andres Ponce
UCSD School of Medicine, La JoUa, CA, USA
Marsh M, Reddy
UCSD School of Medicine, La Jolla, CA, USA
Philippe Roussel
Universite de Lille 2, Lille, France
Rainer Schreiber
Universitat Regensburg, Germany
Carsten Schultz
European Molecular Biology Laboratory, Heidelberg, Germany
Steve B. Shears
N.LE.H.S./N.LH./D.H.S.S., Research Triangle Park, NC, USA
Udicko Szabo
Eberhard-Karls-Universitat Tubingen, Germany
Alexis Traynor-Kaplan
hiologic Lie, Seattle, WA, USA
Frank Thevenot,
Universitat Witten/Herdecke, Witten, Germany.
CONTRIBUTING AUTHORS
Thilo Voelcker
Universitat Regensburg, Germany.
Sabine Wallisch
Eberhard-Karls-Universitat Tubingen, Germany
Ling Yang
N.LE.H.S./N.LH./D.H.S.S., Research Triangle Park, NC, USA.
